Cebocephaly, alobar holoprosencephaly, spina bifida, and sirenomelia in a stillbirth.
نویسندگان
چکیده
Cebocephaly and sirenomelia are uncommon birth defects. Their association is extremely rare; however, the presence of spina bifida with both conditions is not unexpected. We report on a female still-birth with cebocephaly, alobar holoprosencephaly, cleft palate, lumbar spina bifida, sirenomelia, a single umbilical artery, and a 46,XX karyotype, but without maternal diabetes mellitus. Our case adds to the examples of overlapping cephalic and caudal defects, possibly related to vulnerability of the midline developmental field or axial mesodermal dysplasia spectrum.
منابع مشابه
Alobar holoprosencephaly associated with cebocephaly and craniosynostosis.
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ورودعنوان ژورنال:
- Journal of medical genetics
دوره 34 3 شماره
صفحات -
تاریخ انتشار 1997